alpha-Galactosidase A/GLA Antibody

Galactosidase alpha encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq]

This product is for research use only and is not approved for use in humans or in clinical diagnosis. Primary Antibodies are guaranteed for 1 year from date of receipt.

We have publications tested in 1 confirmed species: Mouse.

We have publications tested in 1 application: IF/IHC.

Showing Publication 1 - 1 of 1.

Publication using NBP1-89796	Applications	Species
Su Xu, Yi Lun, Nastry Brignol et al. Coformulation of a Novel Human alpha-Galactosidase A With the Pharmacological Chaperone AT1001 Leads to Improved Substrate Reduction in Fabry Mice. Molecular Therapy 2015-04-27 [PMID: 25915924] (IF/IHC, Mouse)	IF/IHC	Mouse

Array NBP1-89796

• alpha-Galactosidase A/GLA Antibodies
• alpha-Galactosidase A/GLA Antibody Pair
• alpha-Galactosidase A/GLA ELISA Kits
• alpha-Galactosidase A/GLA Lysate
• alpha-Galactosidase A/GLA Proteins
• alpha-Galactosidase A/GLA Proteins and Enzyme