Research of Isovaleryl-coa Dehydrogenase Deficiency has been linked to Acidemia, Inborn Errors Of Metabolism, Methylmalonic Acidemia, Propionic Acidemia, Maple Syrup Urine Disease. The study of Isovaleryl-coa Dehydrogenase Deficiency has been mentioned in research publications which can be found using our bioinformatics tool below. Researched pathways related to Isovaleryl-coa Dehydrogenase Deficiency include Excretion, Fatty Acid Oxidation, Urea Cycle, Conjugation, Translation. These pathways complement our catalog of research reagents for the study of Isovaleryl-coa Dehydrogenase Deficiency including antibodies and ELISA kits against MEDIUM-CHAIN ACYL-COA DEHYDROGENASE, LONG-CHAIN ACYL-COA DEHYDROGENASE, 3-HYDROXY-3-METHYLGLUTARYL-COENZYME A LYASE, ACAA1, ACADS.
Top Research Reagents
We have 1249 products for the study of Isovaleryl-coa Dehydrogenase Deficiency that can be applied to Chromatin Immunoprecipitation, Chromatin Immunoprecipitation (ChIP), Flow Cytometry, Immunocytochemistry/ Immunofluorescence, Immunohistochemistry, Western Blot from our catalog of antibodies and ELISA kits.
![Western Blot: EPB42 Antibody (2G12) [H00002038-M01] - Analysis of EPB42 expression in transfected 293T cell line by EPB42 monoclonal antibody (M01), clone 2G12.Lane 1: EPB42 transfected lysate(69.5 KDa).Lane 2: Non-transfected lysate.](https://images.novusbio.com/fullsize/EPB42-Antibody-2G12-Western-Blot-H00002038-M01-img0005.jpg)
![Immunocytochemistry/Immunofluorescence: EPB42 Antibody (2G12) [H00002038-M01] - Analysis of monoclonal antibody to EPB42 on HeLa cell . Antibody concentration 10 ug/ml.](https://images.novusbio.com/fullsize/EPB42-Antibody-2G12-Immunocytochemistry-Immunofluorescence-H00002038-M01-img0003.jpg)
![Western Blot: Nbs1 Antibody [NB100-143] - Lysates of HeLa human cervical epithelial carcinoma parental cell line and Nbs1 knockout (KO) HeLa cell line. PVDF membrane was probed with 1:1000 of Rabbit Anti-Human Polyclonal [NB100-143] followed by HRP-conjugated Anti-Rabbit IgG Secondary Antibody (HAF008). Specific band was detected for Nbs1 at approximately 95 kDa (as indicated) in the parental HeLa cell line, but is not detectable in the knockout HeLa cell line. This experiment was conducted under reducing conditions.](https://images.novusbio.com/fullsize/Nbs1-Antibody-Knockout-Validated-NB100-143-img0015.jpg)
![Western Blot: Nbs1 Antibody [NB100-143] - Western Blot with Nbs1 Antibody [NB100-143]. KSHV LANA recruits MRN (Mre11-Rad50-NBS1) complex. Co-immunoprecipitation of endogenous LANA and MRN proteins in BC3 cells. Cells were lysed using TBS-T buffer and the cell lysate was incubated with benzonase. After centrifugation, supernatant was incubated overnight with anti-LANA or IgG-control beads. The precipitated complexes were analyzed for the presence of endogenous Rad50, Mre11 and NBS1 by SDS-PAGE and immunoblotting. Image collected and cropped by CiteAb from the following publication (https://dx.plos.org/10.1371/journal.ppat.1006335), licensed under a CC-BY license.](https://images.novusbio.com/fullsize/Nbs1-Antibody-Western-Blot-NB100-143-img0016.jpg)
![Western Blot: HMGCL Antibody [NBP1-32767] - rat liver lysate/extract 10 % SDS-PAGE gel, antibody dilution 1:10000.](https://images.novusbio.com/fullsize/HMGCL-Antibody-Western-Blot-NBP1-32767-img0007.jpg)
![Immunocytochemistry/Immunofluorescence: HMGCL Antibody [NBP1-32767] - HeLa cells were fixed in ice-cold MeOH for 5 min. Green: HMGCL protein stained by HMGCL antibody diluted at 1:500. Blue: Hoechst 33342 staining. Scale bar = 10 um.](https://images.novusbio.com/fullsize/HMGCL-Antibody-Immunocytochemistry-Immunofluorescence-NBP1-32767-img0008.jpg)
![Western Blot: Pancreatic Amylase Alpha Antibody (6D4) [NBP1-47659] - Pancreatic Amylase Alpha Antibody (6D4) HEK293T cells were transfected with the pCMV6-ENTRY control (Left lane) or pCMV6-ENTRY Pancreatic Amylase(Right lane) cDNA for 48 hrs and lysed. Equivalent amounts of cell lysates (5 ug per lane) were separated by SDS-PAGE and immunoblotted with anti-Pancreatic Amylase.](https://images.novusbio.com/fullsize/Pancreatic-Amylase-Alpha-Antibody-6D4-Western-Blot-NBP1-47659-img0022.jpg)
![Immunohistochemistry-Paraffin: Pancreatic Amylase Alpha Antibody (6D4) [NBP1-47659] - Pancreatic Amylase Alpha Antibody (6D4) Staining of paraffin-embedded ovary using anti-Pancreatic Amylase mouse monoclonal antibody.](https://images.novusbio.com/fullsize/Pancreatic-Amylase-Alpha-Antibody-6D4-Immunohistochemistry-Paraffin-NBP1-47659-img0021.jpg)
![Western Blot: NME1-NME2 Antibody [NBP1-80992] - Western blot analysis in mouse cell line NIH-3T3, rat cell line NBT-II and rat cell line pC12.](https://images.novusbio.com/fullsize/NME1-NME2-Antibody-Western-Blot-NBP1-80992-img0011.jpg)
![Immunocytochemistry/Immunofluorescence: NME1-NME2 Antibody [NBP1-80992] - Immunofluorescent staining of human cell line A-431 shows localization to cytosol.](https://images.novusbio.com/fullsize/NME1-NME2-Antibody-Immunocytochemistry-Immunofluorescence-NBP1-80992-img0010.jpg)
![Western Blot: HADHB Antibody [NBP1-82609] - Generation of NIH 3T3 HADHB KO Cell Lines by CRISPR/Cas9(A) Western blot analysis of HADHB protein levels in two HADHB KO clones (AQ and Z) compared with decreasing amounts of total protein extract from WT NIH 3T3 cells. Image collected and cropped by CiteAb from the following publication (https://linkinghub.elsevier.com/retrieve/pii/S2162253118303135) licensed under a CC-BY license.](https://images.novusbio.com/fullsize/HADHB-Antibody-Knockout-Validated-NBP1-82609-img0016.jpg)
![Immunohistochemistry: HADHB Antibody [NBP1-82609] - (B) IHC staining of murine adductor muscle after ischemia induction revealed expression of HADHB, predominantly in the cytoplasm of cells. (D) Microarray analysis of mRNA expression of HADHB mRNA in the adductor muscle of mice at several time points after induction of ischemia (4 mice per time point). (E) Western blot showing HADHB levels in murine adductor muscle tissue on day 0, 1, and 3 after hindlimb ligation. For each time point, samples from right (R) unligated paws and left (L) ligated paws are presented next to each other. Tubulin was used as a loading control. (F) Quantification of the western blot. The HADHB signal was normalized against tubulin. Each bar represents a biological triplicate and technical duplicate. Image collected and cropped by CiteAb from the following publication (https://linkinghub.elsevier.com/retrieve/pii/S2162253118303135) licensed under a CC-BY license.](https://images.novusbio.com/fullsize/HADHB-Antibody-Immunohistochemistry-NBP1-82609-img0015.jpg)
![Immunohistochemistry-Paraffin: ACAA1 Antibody [NBP1-85786] - Analysis in human liver and pancreas tissues using NBP1-85786 antibody. Corresponding ACAA1 RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/ACAA1-Antibody-Immunohistochemistry-Paraffin-NBP1-85786-img0013.jpg)
![Western Blot: ACAA1 Antibody [NBP1-85786] - Analysis using Anti-ACAA1 antibody NBP1-85786 (A) shows similar pattern to independent antibody NBP1-86128 (B).](https://images.novusbio.com/fullsize/ACAA1-Antibody-Western-Blot-NBP1-85786-img0011.jpg)
![Immunohistochemistry-Paraffin: AUH Antibody [NBP1-86516] - Staining of human pancreas shows low expression as expected.](https://images.novusbio.com/fullsize/AUH-Antibody-Immunohistochemistry-Paraffin-NBP1-86516-img0005.jpg)
![Immunohistochemistry: AUH Antibody [NBP1-86516] - Staining of human stomach shows strong cytoplasmic positivity in glandular cells.](https://images.novusbio.com/fullsize/AUH-Antibody-Immunohistochemistry-NBP1-86516-img0003.jpg)
![Immunohistochemistry-Paraffin: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Staining in human liver and kidney tissues . Corresponding OTC RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/Ornithine-Carbamoyltransferase-Antibody-Immunohistochemistry-Paraffin-NBP1-87408-img0020.jpg)
![Immunohistochemistry-Paraffin: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Staining of human cerebral cortex, kidney, liver and small intestine using Anti-OTC antibody NBP1-87408 (A) shows similar protein distribution across tissues to independent antibody NBP1-88121 (B).](https://images.novusbio.com/fullsize/Ornithine-Carbamoyltransferase-Antibody-Immunohistochemistry-Paraffin-NBP1-87408-img0027.jpg)
![Immunohistochemistry-Paraffin: ACADS Antibody [NBP1-89290] - Analysis in human duodenum and tonsil tissues. Corresponding ACADS RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/ACADS-Antibody-Immunohistochemistry-Paraffin-NBP1-89290-img0017.jpg)
![Western Blot: ACADS Antibody [NBP1-89290] - Lane 1: NIH-3T3 cell lysate (Mouse embryonic fibroblast cells)<br/>Lane 2: NBT-II cell lysate (Rat Wistar bladder tumour cells)](https://images.novusbio.com/fullsize/ACADS-Antibody-Western-Blot-NBP1-89290-img0004.jpg)
![Western Blot: Pallidin Antibody (1H9) [NBP2-01763] - HEK293T cells were transfected with the pCMV6-ENTRY control (Left lane) or pCMV6-ENTRY Pallidin (Right lane) cDNA for 48 hrs and lysed. Equivalent amounts of cell lysates (5 ug per lane) were separated by SDS-PAGE and immunoblotted with anti-Pallidin.](https://images.novusbio.com/fullsize/Pallidin-Antibody-1H9-Western-Blot-NBP2-01763-img0007.jpg)
![Immunohistochemistry-Paraffin: Pallidin Antibody (1H9) [NBP2-01763] - Staining of paraffin-embedded Human tonsil using anti-Pallidin mouse monoclonal antibody.](https://images.novusbio.com/fullsize/Pallidin-Antibody-1H9-Immunohistochemistry-Paraffin-NBP2-01763-img0006.jpg)
![Western Blot: IVD Antibody (1B10) [NBP2-03047] Analysis of extracts (35ug) from 9 different cell lines by using anti-IVD monoclonal antibody.](https://images.novusbio.com/fullsize/IVD-Antibody-1B10-Western-Blot-NBP2-03047-img0004.jpg)
![Immunocytochemistry/Immunofluorescence: IVD Antibody (1B10) [NBP2-03047] - Staining of COS7 cells transiently transfected by pCMV6-ENTRY IVD.](https://images.novusbio.com/fullsize/IVD-Antibody-1B10-Immunocytochemistry-Immunofluorescence-NBP2-03047-img0003.jpg)
![SDS-Page: PRH1 Protein [NBP2-23368]](https://images.novusbio.com/fullsize/PRH1-Protein-SDS-Page-NBP2-23368-img0001.jpg)
![N/A Complement Component C5a [Biotin]](https://images.novusbio.com/fullsize2/DATA_Complement_Component_C5a_DY2150_ELISA_1774.jpg)
![Western Blot: ACAA2 Antibody (OTI1C10) [NBP2-46477] - Analysis of extracts (35ug) from 9 different cell lines (HepG2: human; HeLa: human; SVT2: mouse; A549: human; COS7: monkey; Jurkat: human; MDCK: canine; PC12: rat; MCF7: human).](https://images.novusbio.com/fullsize/ACAA2-Antibody-OTI1C10-Western-Blot-NBP2-46477-img0009.jpg)
![Immunohistochemistry: ACAA2 Antibody (OTI1C10) [NBP2-46477] - Analysis of Human endometrium tissue. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 120C for 3min)](https://images.novusbio.com/fullsize/ACAA2-Antibody-OTI1C10-Immunohistochemistry-NBP2-46477-img0007.jpg)
![Western Blot: TEAD2 Antibody [NBP2-94220] -Analysis of lysates from wild type (WT) and 293T cells transfected with TEAD2 using TEAD1/2/3/4 mAb at 1:1000 dilution. Secondary antibody:HRP Goat Anti-Rabbit IgG (H+L) at 1:10000 dilution.Lysates/proteins: 25 ug per lane.Blocking buffer: 3% nonfat dry milk in TBST.Detection:ECL Basic Kit. Exposuretime: 20s.](https://images.novusbio.com/fullsize/nbp2-94220_rabbit-polyclonal-tead2-antibody-western-blot-110202410413..jpg)
![Western Blot: TEAD2 Antibody [NBP2-94220] -Analysis of lysates from wild type (WT) and 293F cells transfected with TEAD3 using TEAD1/2/3/4 mAb at 1:1000 dilution. Secondary antibody:HRP Goat Anti-Rabbit IgG (H+L) at 1:10000 dilution.Lysates/proteins: 25 ug per lane.Blocking buffer: 3% nonfat dry milk in TBST.Detection:ECL Basic Kit.Exposuretime: 10s.](https://images.novusbio.com/fullsize/antibody/nbp2-94220_rabbit-polyclonal-tead2-antibody-western-blot-110202410551..jpg)
![SDS-Page: Recombinant Human PRH2 Protein [H00005555-P01] - 12.5% SDS-PAGE Stained with Coomassie Blue.](https://images.novusbio.com/fullsize/qc_test-H00005555-P01-1.jpg)
