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Phenylalanine Hydroxylase Products

Antibodies
Phenylalanine Hydroxylase Ant ...
Phenylalanine Hydroxylase Antibody
NBP2-48615
Species: Hu, Mu, Rt
Applications: WB, IHC
Host: Rabbit Polyclonal
Phenylalanine Hydroxylase Ant ...
Phenylalanine Hydroxylase Antibody
NBP1-80917
Species: Hu
Applications: WB, IHC
Host: Rabbit Polyclonal
Phenylalanine Hydroxylase Ant ...
Phenylalanine Hydroxylase Antibody...
NBP3-32708
Species: Hu, Mu, Rt
Applications: WB, Flow, IHC
Host: Rabbit Monoclonal
ELISA Kits
Human Phenylalanine Hydroxyla ...
Human Phenylalanine Hydroxylase EL...
NBP2-81206
Species: Hu
Applications: ELISA
Proteins
Recombinant Human Phenylalani ...
Recombinant Human Phenylalanine Hy...
H00005053-P01
Species: Hu
Applications: WB, ELISA, MA, PAGE, AP
Phenylalanine Hydroxylase Rec ...
Phenylalanine Hydroxylase Recombin...
NBP1-80917PEP
Species: Hu
Applications: AC
Phenylalanine Hydroxylase Rec ...
Phenylalanine Hydroxylase Recombin...
NBP2-48615PEP
Species: Hu
Applications: AC

Description

PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria.

Bioinformatics

Uniprot Human
Human
Human
Product By Gene ID 5053
Alternate Names
  • EC 1.14.16
  • EC 1.14.16.1
  • PH
  • phe-4-monooxygenase
  • Phe-4-monooxygenase
  • phenylalanine 4-monooxygenase
  • phenylalanine hydroxylase
  • phenylalanine-4-hydroxylase
  • PKU
  • PKU1