Species: Hu, Mu, Rt
Applications: WB, IHC, KD
Host: Rabbit Polyclonal
Species: Hu, Mu, Rt, Bv
Applications: WB, Simple Western, ICC/IF, IHC, IP
Host: Rabbit Polyclonal
Species: Hu, Mu, Rt
Applications: WB, ICC/IF, IHC
Host: Rabbit Polyclonal
Species: Hu
Applications: ELISA
Species: Hu
Applications: ELISA
Species: Hu
Applications: AC
Species: Hu
Applications: AC
Description
The enzyme system for cleavage of glycine (glycine cleavage system; GCS; EC 2.1.2.10), which is confined to themitochondria, is composed of 4 protein components: P protein (a pyridoxal phosphate-dependent glycine decarboxylase),H protein (a lipoic acid-containing protein), T protein (a tetrahydrofolate-requiring enzyme), and L protein (alipoamide dehydrogenase). Glycine encephalopathy (GCE; MIM 605899) may be due to a defect in any one of these enzymes;see MIM 238310, MIM 238330, and MIM 238331.(supplied by OMIM)
Bioinformatics
| Entrez |
Human
|
| Uniprot |
Human
|
| Product By Gene ID |
2731 |
| Alternate Names |
- EC 1.4.4.2
- GCE
- GCSPMGC138198
- Glycine cleavage system P protein
- glycine cleavage system protein P
- glycine decarboxylase P-protein
- Glycine decarboxylase
- glycine dehydrogenase (decarboxylating)
- glycine dehydrogenase (decarboxylating; glycine decarboxylase, glycine cleavagesystem protein P)
- glycine dehydrogenase [decarboxylating], mitochondrial
- HYGN1
- MGC138200
- NKH
|
